A Rare Case of Encephalotrigeminal Angiomatosis: A Case Report
Keywords:Encephalotrigeminal angiomatosis, port wine stain, tram-track calcifications
Aim: Sturge–Weber Syndrome, also known as encephalotrigeminal angiomatosis, is an uncommon, nonhereditary developmental anomaly.
Methodology: A 48-year-old woman presented for routine dental treatment. She had a history of seizures and had a port wine stain on the right side of her face, which followed the distribution of the trigeminal nerve. Skull radiographs revealed “tram-track” calcifications.
Conclusions: The early diagnosis of Sturge–Weber Syndrome requires a multidisciplinary approach. Oral health care professionals need adequate knowledge and understanding of the disease process to help diagnose and treat these patients.
How to cite this article: Jacob LE, Mathew AL, Omal PM, Abraham T, Thomas J, Varghese S. A Rare Case of Encephalotrigeminal Angiomatosis – A Case Report Int Dent Res 2017;7:13-6.
Linguistic Revision: The English in this manuscript has been checked by at least two professional editors, both native speakers of English.