A Rare Case of Encephalotrigeminal Angiomatosis: A Case Report

  • Lisa Elizabeth Jacob Pushpagiri College of Dental Sciences, Department of Oral Medicine and Radiology, Tiruvalla, Kerala, South India.
  • Anuna Laila Mathew Pushpagiri College of Dental Sciences, Department of Oral Medicine and Radiology, Tiruvalla, Kerala, South India.
  • Omal Pattali Mohanan Pushpagiri College of Dental Sciences, Department of Oral Medicine and Radiology, Tiruvalla, Kerala, South India.
  • Thomas Abraham Pushpagiri College of Dental Sciences, Department of Oral Medicine and Radiology, Tiruvalla, Kerala, South India.
  • Jerin Thomas Pushpagiri College of Dental Sciences, Department of Oral Medicine and Radiology, Tiruvalla, Kerala, South India.
  • Stephy Varghese Pushpagiri College of Dental Sciences, Department of Oral Medicine and Radiology, Tiruvalla, Kerala, South India.
Keywords: Encephalotrigeminal angiomatosis, port wine stain, tram-track calcifications

Abstract

Aim: Sturge–Weber Syndrome, also known as encephalotrigeminal angiomatosis, is an uncommon, nonhereditary developmental anomaly.

Methodology: A 48-year-old woman presented for routine dental treatment. She had a history of seizures and had a port wine stain on the right side of her face, which followed the distribution of the trigeminal nerve. Skull radiographs revealed “tram-track” calcifications.

Conclusions: The early diagnosis of Sturge–Weber Syndrome requires a multidisciplinary approach. Oral health care professionals need adequate knowledge and understanding of the disease process to help diagnose and treat these patients. 

How to cite this article: Jacob LE, Mathew AL, Omal PM, Abraham T, Thomas J, Varghese S. A Rare Case of Encephalotrigeminal Angiomatosis – A Case Report Int Dent Res 2017;7:13-6.

Linguistic Revision: The English in this manuscript has been checked by at least two professional editors, both native speakers of English.

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Published
2017-04-15
How to Cite
Jacob, L., Mathew, A., Mohanan, O., Abraham, T., Thomas, J., & Varghese, S. (2017). A Rare Case of Encephalotrigeminal Angiomatosis: A Case Report. International Dental Research, 7(1), 13-16. https://doi.org/10.5577/intdentres.2017.vol7.no1.3